Title

Rare cause of infranodal block

Aurora Affiliations

Aurora Sinai/Aurora St. Luke's Medical Centers

Abstract

The patient exhibits multiple features suggestive of Timothy syndrome, which is a multisystem autosomal-dominant condition with findings that include prolonged QT interval, hand and foot abnormalities, dysmorphic facial features, and mental retardation. A 2:1 infranodal atrioventricular block may occasionally be seen in the setting of severely prolonged QT interval. Functional nature of atrioventricular block is demonstrated by resumption of 1:1 conduction with changes in heart rate.

Document Type

Article

PubMed ID

27837893

DOI

10.1016/j.ccep.2016.07.005